内容摘要：Batten Disease Family Association chief executive, Liz Brownnutt, said the organisation supported 117 children and young adults with Batten disease in the UK, four in Wales.

Batten Disease Family Association chief executive, Liz Brownnutt, said the organisation supported 117 children and young adults with Batten disease in the UK, four in Wales.

The Wilson Arms, in Coniston, in the Lake District, was first told to remove its four tubs by the Lake District National Park Authority (LDNP) in July 2022, which the pub’s co-owner subsequently appealed.But government planners ruled against Matthew Mayver’s appeal and said the development harmed the appearance of the area.

Mr Mayvers called the whole situation a “farce”. The LDNP said it hoped to see legal compliance from the owner.The Wilson Arms has shepherds huts, "glamping" pods and cottages for guests to stay in, as well as hotel rooms.The pub owner admitted he was partly to blame for the situation.

“I didn’t realise you needed planning permission for a hot tub,” Mr Mayvers said.After the LDNP reached out in 2022, Mr Mayvers said he had made a mistake and would send off a planning application for the tubs.

But as the regulatory body had already ruled against the tubs, they could not accept the new application, according to Mr Mayvers.

He then appealed the decision with the government's Planning Inspectorate, who responded on 5 April and backed the LDNP’s verdict.Whenever she is alone, walking in the forest, she will worry about her children, she says.

“I will keep trying, until I can’t any more,” she says. “Because I think that one day, my children will say: ‘My mum worked so hard. She went through what she went through for us, and she never gave up.’”names 100 inspiring and influential women around the world every year. Follow BBC 100 Women on

. Join the conversation usingRosie Duffield has told the BBC that Sir Keir Starmer’s team cares "more about greed and power than making a difference" in her first broadcast interview since resigning from the Labour Party.